Pulmonary Artery Hypertension (PAH) is a life-threatening condition in which the blood pressure in the pulmonary artery rises above normal levels, leading to the heart working harder to force blood to the lungs. PAH can be caused by a variety of conditions, such as idiopathic (no obvious cause), birth defect, connective tissue disease, HIV, drug and alcohol use, liver disease, and some forms of cancer.

PAH is a progressive condition, and can worsen over time if not treated properly. Symptoms of PAH include difficulty breathing, tiredness and fatigue, chest pain, lightheadedness, rapid heartbeat, swelling in the feet and legs, and dizziness. Unfortunately, the majority of patients with PAH are not diagnosed until their condition is quite advanced, which can make it difficult to manage.

The goals of PAH treatment are to reduce symptoms, improve quality of life, and prevent or delay disease progression. Treatment plans may include lifestyle changes, such as avoiding alcohol or drug use and limiting salt intake, as well as medications, such as phosphodiesterase inhibitors, prostanoids, or endothelin antagonists. In some cases, a patient may require surgery or a lung transplant to improve their prognosis.

It is important to speak to your doctor about any symptoms you may have that could indicate PAH, as early diagnosis and treatment can help to slow the progression of the disease. PAH can be a difficult condition to deal with, but with the right treatment and care, patients can often lead normal, productive lives.

By following a treatment plan and making lifestyle modifications, such as quitting smoking, engaging in regular exercise and eating a balanced, low-salt diet, people living with PAH can remain healthy and prolong their lives. PAH is a serious condition, but with the right care and attention, patients can often achieve good control of the disease and enjoy a good quality of life.